A case of hemolytic-uremic syndrome with the development of catastrophic antiphospholipid syndrome: Diagnosis and clinical tactics

  • Authors: Dzhumabaeva B.T.1, Biryukova L.S.1, Tsvetaeva N.V.1, Sukhanova G.A.1, Vasil'ev S.A.1, Shavlokhov V.S.1, Karagyulyan S.R.1, Kaplanskaya I.B.1, Petrova V.I.1, Avdonin P.V.1, Dzhumabayeva BT1, Biryukova LS1, Tsvetayeva NV1, Sukhanova GA1, Vasilyev SA1, Shavlokhov VS1, Karagyulyan SR1, Kaplanskaya IB1, Petrova VI1, Avdonin PV1
  • Affiliations:
  • Issue: Vol 82, No 3 (2010)
  • Pages: 56-60
  • Section: Editorial
  • URL: https://ter-arkhiv.ru/0040-3660/article/view/30573
  • Cite item

Abstract


The paper describes a case of practically simultaneous development of the hemolytic-uremic syndrome (HUS) and the catastrophic antiphospholipid syndrome (CAPS) complicated by mesenteric vessel thrombosis and small bowel necrosis. Multimodality treatment comprising volume plasmapheresis, fresh frozen plasma transfusion, hemodialysis, anticoagulant and disaggregant therapy could relieve thrombogenic events, such as pulmonary artery thromboembolism and intestinal necrosis.

About the authors

Boldukyz Tolgonbaevna Dzhumabaeva

Email: bola@blood.ru

Lyudmila Semenovna Biryukova

Email: birjukova@blood.ru

Nina Valentinovna Tsvetaeva

Email: ntsvet@blood.ru

Galina Aleksandrovna Sukhanova

Email: galsuhan@mail.ru

Sergey Aleksandrovich Vasil'ev

Email: vasiliev@blood.ru

Viktor Sergeevich Shavlokhov

Email: shavlohov@mail.ru

Suren Rolandovich Karagyulyan

Email: krz@blood,ru

Irina Borisovna Kaplanskaya

Email: irinak@blood.ru

Vera Ivanovna Petrova

Pavel Vladimirovich Avdonin

Email: pvavdonin@yandex.ru

B T Dzhumabayeva

L S Biryukova

N V Tsvetayeva

G A Sukhanova

S A Vasilyev

V S Shavlokhov

S R Karagyulyan

I B Kaplanskaya

V I Petrova

P V Avdonin

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