Hereditary spherocytic hemolytic anemia in an adult with the formation of ectopic foci of extramedullary hemopoiesis in the chest


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Abstract

The paper describes a rare case of formation of paravertebral extramedullary hemopoietic foci in microspherocytic anemia or Minkovsky-Shoffar disease in an adult.
Therapeutic splenectomy has led to regression of extramedullary hemopoietic foci, which supports that there is a direct relationship of the above formations to the specific features of the etiology and pathogenesis of microspherocytic anemia.

About the authors

A L Melikyan

Hematology Research Center, Russian Academy of Medical Sciences, Moscow

Email: anoblood@mail.ru
Hematology Research Center, Russian Academy of Medical Sciences, Moscow

E K Egorova

Hematology Research Center, Russian Academy of Medical Sciences, Moscow

Email: helenegorova@mail.ru
Hematology Research Center, Russian Academy of Medical Sciences, Moscow

S R Karagyulyan

Hematology Research Center, Russian Academy of Medical Sciences, Moscow

Hematology Research Center, Russian Academy of Medical Sciences, Moscow

M A Silayev

Hematology Research Center, Russian Academy of Medical Sciences, Moscow

Email: max-blood@mail.ru
Hematology Research Center, Russian Academy of Medical Sciences, Moscow

I B Kaplanskaya

Hematology Research Center, Russian Academy of Medical Sciences, Moscow

Hematology Research Center, Russian Academy of Medical Sciences, Moscow

M K Gitis

Hematology Research Center, Russian Academy of Medical Sciences, Moscow

Email: mgitis@gmail.com
Hematology Research Center, Russian Academy of Medical Sciences, Moscow

S V Kolodei

Hematology Research Center, Russian Academy of Medical Sciences, Moscow

Hematology Research Center, Russian Academy of Medical Sciences, Moscow

L G Kovaleva

Hematology Research Center, Russian Academy of Medical Sciences, Moscow

Email: kovaleva@blood.ru
Hematology Research Center, Russian Academy of Medical Sciences, Moscow

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