Pulmonary hypertension in patients with systemic sclerosis with CREST-syndrome and without it


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Abstract

Aim. To study incidence rate and characteristics of pulmonary hypertension development in patients with systemic sclerosis (SS).
Material and methods. The study included 31 SS patients (30 females, 1 male, age 33-75 years mean age 47.7+1.7 years).
Results. Pulmonary hypertension occurred more frequently in SS patients with CREST-syndrome than in SS patients free of this syndrome. SS patients with CREST-syndrome had also more severe ventricular hypertrophy than ventricular dilation.
Conclusion. Echocardiography proved to be a highly informative method for detection of pulmonary hypertension in patients with SS. The necessity of hemodynamical study in SS patients is emphasized.

About the authors

N A Karoli

A P Rebrov

E E Orlova

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