<?xml version="1.0" encoding="UTF-8"?>
<!DOCTYPE root>
<article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xmlns:ali="http://www.niso.org/schemas/ali/1.0/" article-type="other" dtd-version="1.2" xml:lang="en"><front><journal-meta><journal-id journal-id-type="publisher-id">Terapevticheskii arkhiv</journal-id><journal-title-group><journal-title xml:lang="en">Terapevticheskii arkhiv</journal-title><trans-title-group xml:lang="ru"><trans-title>Терапевтический архив</trans-title></trans-title-group></journal-title-group><issn publication-format="print">0040-3660</issn><issn publication-format="electronic">2309-5342</issn><publisher><publisher-name xml:lang="en">LLC Obyedinennaya Redaktsiya</publisher-name></publisher></journal-meta><article-meta><article-id pub-id-type="publisher-id">33392</article-id><article-categories><subj-group subj-group-type="toc-heading" xml:lang="en"><subject>Editorial article</subject></subj-group><subj-group subj-group-type="toc-heading" xml:lang="ru"><subject>Передовая статья</subject></subj-group><subj-group subj-group-type="article-type"><subject></subject></subj-group></article-categories><title-group><article-title xml:lang="en">Hemolytic anemia due to anomalous unstable hemoglobin BuenosAires</article-title><trans-title-group xml:lang="ru"><trans-title>ГЕМОЛИТИЧЕСКАЯ АНЕМИЯ ВСЛЕДСТВИЕ АНОМАЛЬНОГО НЕСТАБИЛЬНОГОГЕМОГЛОБИНА BUENOS AIRES</trans-title></trans-title-group></title-group><contrib-group><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Rumyantseva</surname><given-names>Yu V</given-names></name><name xml:lang="ru"><surname>Румянцева</surname><given-names>Ю В</given-names></name></name-alternatives><bio xml:lang="ru"><p>НИИ детской гематологии Минздрава РФ</p></bio><xref ref-type="aff" rid="aff1"/></contrib><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Surin</surname><given-names>V L</given-names></name><name xml:lang="ru"><surname>Сурин</surname><given-names>В Л</given-names></name></name-alternatives><bio xml:lang="ru"><p>ГНЦ РАМН</p></bio><xref ref-type="aff" rid="aff2"/></contrib><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Smetanina</surname><given-names>N S</given-names></name><name xml:lang="ru"><surname>Сметанина</surname><given-names>Н С</given-names></name></name-alternatives><bio xml:lang="ru"><p>Российская детская клиническая больница Минздрава РФ, Москва</p></bio><xref ref-type="aff" rid="aff3"/></contrib><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Plyasunova</surname><given-names>S A</given-names></name><name xml:lang="ru"><surname>Плясунова</surname><given-names>С А</given-names></name></name-alternatives><bio xml:lang="ru"><p>Российская детская клиническая больница Минздрава РФ, Москва</p></bio><xref ref-type="aff" rid="aff3"/></contrib><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Blokhina</surname><given-names>L V</given-names></name><name xml:lang="ru"><surname>Блохина</surname><given-names>Л В</given-names></name></name-alternatives><bio xml:lang="ru"><p>Российская детская клиническая больница Минздрава РФ, Москва</p></bio><xref ref-type="aff" rid="aff3"/></contrib><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Kolodei</surname><given-names>S V</given-names></name><name xml:lang="ru"><surname>Колодей</surname><given-names>С В</given-names></name></name-alternatives><bio xml:lang="ru"><p>ГНЦ РАМН</p></bio><xref ref-type="aff" rid="aff2"/></contrib><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Zhirkova</surname><given-names>L V</given-names></name><name xml:lang="ru"><surname>Жиркова</surname><given-names>Л В</given-names></name></name-alternatives><bio xml:lang="ru"><p>Российская детская клиническая больница Минздрава РФ, Москва</p></bio><xref ref-type="aff" rid="aff3"/></contrib></contrib-group><aff-alternatives id="aff1"><aff><institution xml:lang="en"></institution></aff><aff><institution xml:lang="ru">НИИ детской гематологии Минздрава РФ</institution></aff></aff-alternatives><aff-alternatives id="aff2"><aff><institution xml:lang="en"></institution></aff><aff><institution xml:lang="ru">ГНЦ РАМН</institution></aff></aff-alternatives><aff-alternatives id="aff3"><aff><institution xml:lang="en"></institution></aff><aff><institution xml:lang="ru">Российская детская клиническая больница Минздрава РФ, Москва</institution></aff></aff-alternatives><pub-date date-type="pub" iso-8601-date="2003-07-15" publication-format="electronic"><day>15</day><month>07</month><year>2003</year></pub-date><volume>78</volume><issue>7</issue><issue-title xml:lang="en">NO7 (2003)</issue-title><issue-title xml:lang="ru">ТОМ 78, №7 (2003)</issue-title><fpage>78</fpage><lpage>81</lpage><history><date date-type="received" iso-8601-date="2020-04-13"><day>13</day><month>04</month><year>2020</year></date></history><permissions><copyright-statement xml:lang="en">Copyright ©; 2003, Consilium Medicum</copyright-statement><copyright-statement xml:lang="ru">Copyright ©; 2003, ООО "Консилиум Медикум"</copyright-statement><copyright-year>2003</copyright-year><copyright-holder xml:lang="en">Consilium Medicum</copyright-holder><copyright-holder xml:lang="ru">ООО "Консилиум Медикум"</copyright-holder><ali:free_to_read xmlns:ali="http://www.niso.org/schemas/ali/1.0/"/><license><ali:license_ref xmlns:ali="http://www.niso.org/schemas/ali/1.0/">https://creativecommons.org/licenses/by-nc-sa/4.0</ali:license_ref></license></permissions><self-uri xlink:href="https://ter-arkhiv.ru/0040-3660/article/view/33392">https://ter-arkhiv.ru/0040-3660/article/view/33392</self-uri><abstract xml:lang="en"><p/></abstract><trans-abstract xml:lang="ru"><p/></trans-abstract><kwd-group xml:lang="en"><kwd>hemoglobinopathies</kwd><kwd>hemolytic anemia</kwd><kwd>unstable hemoglobin</kwd><kwd>Buenos Aires</kwd><kwd>polymerase chain reaction</kwd><kwd>Buenos Aires</kwd></kwd-group><kwd-group xml:lang="ru"><kwd>гемоглобинопатии</kwd><kwd>гемолитическая анемия</kwd><kwd>нестабильный гемоглобин</kwd><kwd>полимеразная цепная реакция</kwd></kwd-group></article-meta></front><body></body><back><ref-list><ref id="B1"><label>1.</label><mixed-citation>Папаян А. В., Жукова Л. Ю. Анемии у детей. СПб; 2001.</mixed-citation></ref><ref id="B2"><label>2.</label><mixed-citation>А. Г. Румянцев, Ю. Н. Токарев (ред.) Анемии у детей: диагностика и лечение. М.; 2000.</mixed-citation></ref><ref id="B3"><label>3.</label><mixed-citation>Токарев Ю. Н. (ред.) Наследственные анемии и гемоглобинопатии. М.; Медицина; 1983.</mixed-citation></ref><ref id="B4"><label>4.</label><mixed-citation>Меньшиков В. В. Лабораторные методы исследования в клинике. М.: Медицина; 1987. 118-119.</mixed-citation></ref><ref id="B5"><label>5.</label><mixed-citation>Гольдберг Д. И., Гольдберг Е. Д. Справочник по гематологии, 6-е изд. Томск; 1980. 72.</mixed-citation></ref><ref id="B6"><label>6.</label><mixed-citation>Сметанина Н. С., Фарсов Н. Н., Байдун Л. В. и др. Морфологические и биофизические параметры эритроцитов у детей, больных р-талассемией и наследственным сфероцитозом. Гематол. и трансфузиол. 2001; 46 (5): 15-18.</mixed-citation></ref><ref id="B7"><label>7.</label><mixed-citation>Идельсон Л. И. В кн.: Кассирский И. А. (ред.) Справочник по функциональной диагностике. М.: Медицина; 1970. 401.</mixed-citation></ref><ref id="B8"><label>8.</label><mixed-citation>Lee G. R. In: Lee G. R. et al., eds. Wintrobe's clinical hematology. 9-th ed. Philadelphia; London; 1993. 944-964.</mixed-citation></ref><ref id="B9"><label>9.</label><mixed-citation>Тиц Н. (ред.) Энциклопедия клинических лабораторных тестов. ML: Лабинформ; 1997. 127-128.</mixed-citation></ref><ref id="B10"><label>10.</label><mixed-citation>Фирсов Н. Н. Агрегация и дезагрегация эритроцитов: исследование нефелометрическими методами. Соврем. пробл. биомеханики. 1994; 9: 85-97,</mixed-citation></ref><ref id="B11"><label>11.</label><mixed-citation>Poncz M., Solowiejczyk D., Harpel В. et al. Construction of human gene libraries from small amounts of peripheral blood: Analysis of p-like globin genes. Hemoglobin 1982; 6: 27-36.</mixed-citation></ref><ref id="B12"><label>12.</label><mixed-citation>Tagiev A. F., Surin V. L., Gol'tsov A. A. et al. The spectrum of beta-thalassemia mutations in Azerbaijan republic. Hum. Mutat.. 1993; 2: 152-154.</mixed-citation></ref><ref id="B13"><label>13.</label><mixed-citation>Larson P. J., Friedman D. F., Reilly M. P. et al. The presurgical management with erythrocytapheresis of a patient with a high-oxygen-affinity, unstable Hb variant (Hb Bryn Mawr). Transfusion 1997; 37 (7): 703-707.</mixed-citation></ref><ref id="B14"><label>14.</label><mixed-citation>Hiratake S., Komada Y. et al. The first case in Japan of unstable hemoglobin, Hb Buenos Aires [beta 85 (Fl) PheSe'], with parvovirus В19 infection (first case in Japan). Rinsho Ketsueki 1995; 36 (12): 1342-1346.</mixed-citation></ref><ref id="B15"><label>15.</label><mixed-citation>De Weinstein B. I., White J. M., Wiltshire B. G., Lehmann H. A new unstable haemoglobin: Hb Buenos Aires, beta 85 (Fl) Phe leads to Ser. Acta Haematol. (Basel). 1973; 50 (6): 357- 363.</mixed-citation></ref></ref-list></back></article>
