Terapevticheskii arkhivTerapevticheskii arkhiv0040-36602309-5342LLC Obyedinennaya Redaktsiya31018Research ArticlePATHOLOGICAL ANATOMY OF SOME RARE DISEASES OF THE LUNGSChernyaevA L-SamsonovaM V-Research Institute of Pulmonology15032012843596210042020Copyright © 2012, Consilium Medicum2012The article gives a brief review of some rare diseases of the lungs. According to international registers, rare diseases are those which occur in one individual per 2000 population. Brief characteristics, description of pathological anatomy of tumor and other lesions of the lungs are outlined.rare pulmonary diseasespathological anatomyредкие болезни легкихпатологическая анатомия[Windeler J., Lange S. Benefit assessment in special situations rare diseases. Z. Evid. Fortbild. Qual. Gesundhwes. 2008; 102 (1): 25—30.][Cordier J. F. Orphan lung diseases from curiosity to concern. Bull. Acad. Natl. Med. 2004; 188 (5): 755—763.][British Paediatric Orphan Lung Diseases. http://www.bpold.co.uk/.][Australian Lung Foundation Interstitial and Orphan Lung Diseases Registry. http://www.lungfoundation.com.au/media-centre/290.][Rennard S. I. The many "small COPDs" COPD should be an orphan disease. Chest 2008; 134 (3): 623—627.][Rosen S. H., Castleman B., Liebow A. A. Pulmonary alveolar proteinosis. N. Engl. J. Med. 1958; 258: 1123—1142.][Lazor R., Bigay-Game L., Cottin V. et al. Alveolar hemorrhage in anti-basement membrane antibode disease: a series of 28 cases. Medicine (Baltimore). 2007; 86 (3): 181—193.][Feuillet S., Giroux-Leprieur B., Tazi A. Pulmonary Langerhans cell histiocytosis in adults. Presse Med. 2010; 39 (1): 107—115.][Dail D. H., Liebow A. A. Intravascular bronchioloalveolar tumor. Am. J. Pathol. 1975; 78: 6a—7a.][Corrin B., Manners B., Millard M. et al., Histogenesis of theso-called "intravascular bronchioloalveolar tumor". J. Pathol. 1979; 128: 163—167.][Cronin P., Arenberg D. Pulmonary epithelioid hemangioendothelioma: an unusual case and review of literature. Chest 2004; 125: 789—792.][Павлов К. А., Дубова Е. А., Щеголев А. И., Пикунов М. Ю. Эпителиоидная гемангиоэндотелиома легких. Пульмонология 2007; 3: 122—125.][Харченко В. П., Галил-Оглы Г. А., Кузьмин И. В. Онкоморфология легких. М.; 1994.]